COCHLEAR IMPLANTATION IN CHILDREN WITH INNER EAR MALFORMATION AND COCHLEAR NERVE DEFICIENCY

1. Overview
2. Embryology of Inner Ear and Its Malformation
3. Embryology of Cochlear Nerve and Its Deficiency
4. Morphology, Development, and Neurotrophic Regulation of Cochlear Afferent Innervation
5. Genetics of Inner Ear Malformation and Cochlear Nerve Deficiency
6. Classification of Inner Ear Malformations
7. Outcome of Cochlear Implantation in Children with Cochlear Nerve Deficiency and/or Inner Ear Malformations
8. EABR of Inner Ear Malformation and Cochlear Nerve Deficiency After Cochlear Implantation in Children
9. Vestibular Neuropathy
10. Vestibular Development of Children with Inner Ear Malformation and Cochlear Nerve Deficiency
11. Vestibular-Evoked Myogenic Potential After Cochlear Implantion
12. Speech and Hearing after Cochlear Implantation in Children with Inner Ear Malformation and Cochlear Nerve Deficiency

The purpose of this book is to contribute to basic and clinical medical research on cochlear implants for inner ear malformation and cochlear nerve deficiency.
Cochlear implantation for children is performed worldwide, and the outcomes concerning speech and hearing acquisition are epoch-making. However, there are some difficulties associated with applying this operative treatment to patients who have complicated inner ear malformations or cochlear nerve deficiencies that have slowed the development of their speech, hearing, and/or sense of balance.
The first part of the book outlines the fundamental aspects of inner ear maldevelopment to facilitate readers’ understanding of cochlear implantation from the point of view of embryology, morphology, and genetics. In turn, the second part describes current clinical cases and presents successful clinical reports. The book offers a primary resource for otolaryngologists, neurologists, and pediatricians with an interest in this field.

Features
• Highlights current topics regarding cochlear implantation with cognitive inner ear malfunction
• Introduces selected applications and outcomes of difficult clinical cases
• Is written by international specialists in the field of otolaryngology and related disciplines

Author
Kimitaka Kaga, M.D., Ph.D. Emeritus Director, National Institute of Sensory Organs, National Tokyo Medical Center