ORPHAN LUNG DISEASES. A CLINICAL GUIDE TO RARE LUNG DISEASE

- Contains practical and easy-to-access information on the diagnostic approach, with illustrations of chest imaging (mostly high resolution computed tomography).
- Assists the reader in evoking and confirming the diagnosis of a variety of orphan diseases.
- Written by experts internationally.

Focusing on clinical practice, this book explores the less common diseases affecting the airways, systematic disorders with lung involvement, interstitial lung diseases and many other orphan conditions of the lungs. It helps the reader to diagnose and manage these rare orphan diseases. Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease is a practical, informative book written by a team of international authors with much experience in rare pulmonary diseases.
Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease provides synthesized and easily accessible information about the main orphan lung diseases, to aid clinicians in charge of patients with rare disease, or who consider the diagnosis of a rare disease in their patient.

Table of contents (36 chapters)
1.Orphan Lung Diseases from Definition to Organisation of Care
2.The Challenges of Clinical Research in Orphan Diseases
3.Chronic Bronchiolitis in Adults
4. “Diffuse Bronchiectasis of Genetic Origin”
5.Allergic Bronchopulmonary Mycosis
6.Orphan Tracheopathies
7.Amyloidosis and the Respiratory Tract
8.Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss Syndrome): A Clinical and Therapeutic Approach
9.Granulomatosis with Polyangiitis (Wegener’s Granulomatosis)
10.Alveolar Hemorrhage
11.Pulmonary Involvement in Takayasu Arteritis and Behçet Disease
12.Pulmonary Vascular Manifestations of Hereditary Hemorrhagic Telangiectasia
13.Hepatopulmonary Syndrome
14.Non-langerhans Cell Histiocytosis-Including Erdheim-Chester Disease- and the Lung
15.Eosinophilic Pneumonia
16.Multiple Cystic Lung Diseases
17.Lymphangioleiomyomatosis
18.Pulmonary Alveolar Proteinosis
19.Exogenous Lipoid Pneumonia
20.Pulmonary Alveolar Microlithiasis
21.Pulmonary Fibrosis and the Many Faces of UIP
22.The Syndrome of Combined Pulmonary Fibrosis and Emphysema
23.Non-specific, Unclassifiable, and Rare Idiopathic Interstitial Pneumonia: Acute Interstitial Pneumonia, Respiratory Bronchiolitis Interstitial Pneumonia, Desquamative Interstitial Pneumonia, Nonspecific Interstitial Pneumonia
24.Organizing Pneumonias
25.Interstitial Lung Disease in Systemic Sclerosis
26.Interstitial Lung Disease in Connective Tissue Diseases Other Than Systemic Sclerosis
27.Interstitial Lung Disease in Undifferentiated Forms of Connective Tissue Disease
28.Pulmonary Langerhans Cell Histiocytosis and Smoking-Related Interstitial Lung Diseases
29.Rare Causes and the Spectrum of Hypersensitivity Pneumonitis
30.Chronic Beryllium Disease and Other Interstitial Lung Diseases of Occupational Origin
31.Lymphoproliferative Lung Disorders
32.Pulmonary Manifestations of Hematological Malignancies: Focus on Pulmonary Chronic Graft-Versus Host Disease
33.Pulmonary Hypertension in Orphan Lung Diseases
34.Rare and Emergent Drug-Induced and Iatrogenic Respiratory Conditions: A Guide to Their Recognition and Management
35.From Cancer Mimicking Orphan Lung Disease to Orphan Thoracic Oncology
36.Rare Diffuse Lung Diseases of Genetic Origin